hemoglobinopathy

[ˌhiːmoʊˈɡloʊbɪnɒpəθi]
nounfemininepl: hemoglobinopathies / hemoglobinopatias
hemoglobinopatia
1. A genetic disorder affecting the structure or production of hemoglobin, the protein in red blood cells that carries oxygen
Sickle cell disease is one of the most common hemoglobinopathies worldwide.
A doença falciforme é uma das hemoglobinopatias mais comuns no mundo.
2. Any inherited condition resulting from abnormal hemoglobin synthesis or function
Thalassemia is a hemoglobinopathy characterized by reduced hemoglobin production.
A talassemia é uma hemoglobinopatia caracterizada pela produção reduzida de hemoglobina.
This is primarily a medical and scientific term used by healthcare professionals, hematologists, and geneticists. In Brazil, hemoglobinopatias are significant public health concerns, particularly sickle cell disease (doença falciforme), which affects predominantly Afro-Brazilian populations. The term is standardized across both Brazilian and European Portuguese medical communities and is used identically in formal medical contexts in both regions.
Synonyms / Sinônimos
hemoglobin disorderblood disorderinherited hemoglobin disease

Regional Variations

General Brazilian
hemoglobinopatia
Standard medical term used across Brazil in clinical and academic contexts
Portugal
hemoglobinopatia
Same standard term used in European Portuguese medical terminology
USA
hemoglobinopathy
Standard term in American medical practice and literature

Related Words

hemoglobinsickle cell diseasethalassemiaerythrocytegenetic disorderhematology
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